Malignant Peripheral Nerve Sheath Tumour of the Ovary XD01-XD02
Dr. Nobin Babu Kalappurayil,
Kalappurayil, Florican Road, Karaparamba PO, Kozhikode, Kerala-673010, India.
Malignant Peripheral Nerve Sheath Tumour (MPNST) of the ovary is a rare disease, and we hereby describe this entity in a 51-year-old lady who presented with an ovarian mass and disseminated peritoneal disease. She was treated initially with Neo Adjuvant Chemotherapy (NACT) thinking it to be a surface epithelial ovarian tumour and subsequently underwent interval cyto reduction. The nerve sheath origin was confirmed by Immunohistochemistry (IHC) studies. There are no standard treatment guidelines for this rare tumour of the ovary.