Journal of Clinical and Diagnostic Research, ISSN - 0973 - 709X

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Case report
Year : 2017 | Month : October | Volume : 11 | Issue : 10 | Page : OD01 - OD02

Idiopathic Systemic Capillary Leak Syndrome: A Diagnostic Challenge and Its Management

Janak Tarun Bahirwani, Raja Naga Mahesh Maddala, Weena Stanley, Mukhyaprana Prabhu

1. Undergraduate Student, Department of General Medicine, Kasturba Medical College, Manipal, Karnataka, India. 2. Senior Resident, Department of General Medicine, Kasturba Medical College, Manipal, Karnataka, India. 3. Associate Professor, Department of General Medicine, Kasturba Medical College, Manipal, Karnataka, India. 4. Professor, Department of General Medicine, Kasturba Medical College, Manipal, Karnataka, India.

Correspondence Address :
Dr. Janak Tarun Bahirwani,
4, Jawahar Nagar, Prenderghast Road, Secunderabad-500003, Hyderabad, Telangana, India.
E-mail: janaktb@gmail.com

Abstract

Idiopathic Systemic Capillary Leak Syndrome (ISCLS) is a fatal disorder characterised by recurrent episodes of hypotension, hypoalbuminemia and haemoconcentration. It is a rare disease, underreported partly because of unawareness of treating physician. Here is a description of a 30 year old male presenting with history of fever, generalized oedema progressing to hypovolemic shock and multi organ dysfunction. His laboratory studies showed haemoconcenration, hypoalbuminemia and monoclonal gammopathy with negative bacteriological cultures. After excluding other probable etiologies he was diagnosed to have ISCLS. He was managed successfully with intravenous methylprednisolone, theophylline and other supportive measures. He has been put on prophylactic oral theophylline for one year.

Keywords

Hypovolemic shock, Theophylline, Steroids

How to cite this article :

Janak Tarun Bahirwani, Raja Naga Mahesh Maddala, Weena Stanley, Mukhyaprana Prabhu. IDIOPATHIC SYSTEMIC CAPILLARY LEAK SYNDROME: A DIAGNOSTIC CHALLENGE AND ITS MANAGEMENT. Journal of Clinical and Diagnostic Research [serial online] 2017 October [cited: 2017 Oct 24 ]; 11:OD01-OD02. Available from
http://jcdr.net/back_issues.asp?issn=0973-709x&year=2017&month=October&volume=11&issue=10&page=OD01-OD02&id=10707

DOI and Others

DOI: 10.7860/JCDR/2017/31384.10707

Date of Submission: Jul 05, 2017
Date of Peer Review: Aug 04, 2017
Date of Acceptance: Aug 24, 2017
Date of Publishing: Oct 01, 2017

FINANCIAL OR OTHER COMPETING INTERESTS: None.

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