Supratentorial Haemangioblastoma without Von Hippel-Lindau Disease – A Rare Case Report with Review of Literature
Published: October 1, 2017 | DOI: https://doi.org/10.7860/JCDR/2017/29520.10767
Salman Tehran Shaikh, Chandrashekhar Eknath Deopujari
1. Neurosurgery Resident, Department of Neurosurgery, Bombay Hospital Institute of Medical Sciences, Mumbai, Maharashtra, India.
2. Head, Department of Neurosurgery, Bombay Hospital Institute of Medical Sciences, Mumbai, Maharashtra, India.
Correspondence
Dr. Salman Tehran Shaikh,
V-1, Row House II, Sector-6, Vashi, Navi Mumbai-400703, Maharashtra, India.
E-mail: shaikhsalman25@gmail.com
Haemangioblastomas are slow-growing, benign and vascular neoplasms of the central nervous system. They are usually infratentorial, occurring either sporadically in approximately 67% of cases or as a manifestation of Von Hippel-Lindau (VHL) disease in approximately 33% of cases. They were first described by Von Hippel in 1895. Haemangioblastoma in the supratentorial compartment is an infrequent occurrence. Only 58 cases of supratentorial haemangioblastoma without Von Hippel-Lindau disease have been reported from 1902 to 2015. This case discusses a left basifrontal supratentorial haemangioblastoma occurring in a young female who presented with headache and blurring of vision without manifestations of VHL disease. Its benign nature and prognosis merited surgical excision as the treatment of choice.
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