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Primary Ewing Sarcoma of Sphenoid Bone with Intracranial Extension:
A Common Tumour at an
Uncommon Location
ED15-ED16
Correspondence
Rawi Agrawal,
305, Ushakunj Apartment, Ambedkar Path, Jagdeopath, Bailey Road-800014, Patna, Bihar, India.
E-mail: agrawalrawi@gmail.com
Primary Ewing Sarcoma of the cranial bone is rare, contributing to only 1% of all Ewing Sarcomas. Primary cranial Ewing Sarcoma occurs most commonly in temporal bone followed by parietal and occipital bones. Sphenoid bone is less commonly involved. We report a case of Ewing Sarcoma of the sphenoid bone with intra-cranial extension in a 20-month-old boy. On CT scan a provisional diagnosis of rhabdomyosarcoma was made. Fine Needle Aspiration Cytology (FNAC) and histopathological examination of core needle biopsy showed small round cell tumour. On Immunohistochemistry (IHC), CD99 (MIC2) and FLI 1 were strongly positive and final diagnosis of Ewing Sarcoma was made. Considering the rarity of this unusual site, we report a case of primary Ewing Sarcoma arising in the sphenoid bone with erosion of adjacent bones and intra-cranial extension.