Mullerian Ducts Remnants in the 46 XY Disorder of Sex Development
Dr. Ashutosh Halder
Associate Professor,Department of Reproductive Biology All India Institute of Medical Sciences,New Delhi 110029(India)Tele:011-26594211,
Objective: The objective of this study was to find out the prevalence of mullerian duct remnants in the 46 XY disorder of sex development due to disorders in androgen synthesis/action.
Methods: Thirty eight cases of 46 XY disorder of sex development of disorders in androgen synthesis/action were evaluated for diagnosis and management, including mullerian duct remnants. Mullerian ducts remnants were found in nine of them (23.7%). The diagnostic evaluation consisted of pelvic ultrasonography, genitography, cystourethroscopy, genitoscopy and laparoscopy or laparotomy.
Results: The common types were an abnormally large prostatic utricle communicating with the urethra and a rudimentary uterus.
Conclusion: It is concluded that mullerian ducts remnants are common with the 46 XY disorder of sex development due to disorders in androgen synthesis/action. During evaluation of patients, this aspect should be kept in mind and during management, appropriate measures should be undertaken to prevent future complications like chronic urinary tract infections, stones and voiding troubles.