Supratentorial Haemangioblastoma without Von Hippel-Lindau Disease – A Rare Case Report with Review of Literature
Dr. Salman Tehran Shaikh,
V-1, Row House II, Sector-6, Vashi, Navi Mumbai-400703, Maharashtra, India.
Haemangioblastomas are slow-growing, benign and vascular neoplasms of the central nervous system. They are usually infratentorial, occurring either sporadically in approximately 67% of cases or as a manifestation of Von Hippel-Lindau (VHL) disease in approximately 33% of cases. They were first described by Von Hippel in 1895. Haemangioblastoma in the supratentorial compartment is an infrequent occurrence. Only 58 cases of supratentorial haemangioblastoma without Von Hippel-Lindau disease have been reported from 1902 to 2015. This case discusses a left basifrontal supratentorial haemangioblastoma occurring in a young female who presented with headache and blurring of vision without manifestations of VHL disease. Its benign nature and prognosis merited surgical excision as the treatment of choice.