Gorham's Syndrome Associated with Chiari I Malformation and Recurrent Meningitis without Fistula: Case Report PD17-PD19
Frederico Lima Gibbon,
Av. Major Carlos Pinto 123, Casa 14, Rio Grande, Rio Grande do Sul, Brazil.
Gorhamâ€™s syndrome is a rare osteolytic disease in which progressive and spontaneous resorption of bone occurs. We present a case of a boy who presented with Chiari I malformation and recurrent meningitis without fistula. The patient was submitted to occipital bone biopsy and due to lymphocytic infiltration and intraosseous vascular ectasia the diagnosis of Gorham-Stout Syndrome was made. The patient underwent conservative treatment but, unfortunately he died by cardiorespiratory arrest secondary to atlanto-occipital dislocation. This case emphasizes the rarity of this pathology and the previously unreported association with recurrent meningitis without fistula.