Secondary Cardiac Pleomorphic Rhabdomyosarcoma – A Case Report and Review of Literature
Dr. Sandhya Ilanthodi, Faculty, Dept of Pathology, A.J. Institute of
Medical Sciences, Mangalore-575004, India.
Email: firstname.lastname@example.org, Phone: +91-9611873871
Pleomorphic rhabdomyosarcoma (PRMS) is a rare and controversial tumour of the skeletal muscle phenotype. Although it has been recognized that aggressive soft tissue sarcomas may give rise to cardiac metastases, these manifestations are usually late and clinically silent, they being the prevailing findings in exceptional cases. This report describes the occurrence of a massive cardiac metastasis which was secondary to the PRMS of the lower limbs, for which the patient had undergone amputation.
This manifestation was the cause of rapidly progressive congestive heart failure and together with the unusual occurrence of autoimmune thrombocytopaenia, this led to a difficult patient care with a significantly negative influence on the outcome.